Diagnosis and management of congenital rectourethral fistula in a child with long tubular duplication of the colon and Klippel-Feil syndrome - Abstract

Department of Pediatric Urology, Pediatric Surgery Service, Hospital de Clínicas de Porto Alegre, Brazil.

Master's candidate, Graduate Program in Surgical Sciences, Universidade Federal do Rio Grande do Sul, Porto Alegre, RS, Brazil, 90035-003.

 

 

We describe a unique association of congenital rectourethral fistula with long tubular duplication of the colon in a boy with Klippel-Feil syndrome and Sprengel deformity. He presented with a rectourethral fistula after surgical repair of a tubular duplication of the terminal ileum, colon, and proximal rectum. Preoperative identification of the fistula was challenging and was only achieved after cystoscopy with injection of methylene blue under pressure through Foley catheters placed into the anus and distal stoma of a colostomy. Surgical repair was performed through the posterior sagittal approach. The patient is doing well after 4 years of follow-up.

Written by:
Costa EC, Ferreira CT, Salle JL, Fraga JC.   Are you the author?

Reference: J Pediatr Surg. 2011 Nov;46(11):2184-6.
doi: 10.1016/j.jpedsurg.2011.08.022

PubMed Abstract
PMID: 22075355

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